Status:

COMPLETED

Effectiveness of Pulmozyme in Infants With Cystic Fibrosis

Lead Sponsor:

Nationwide Children's Hospital

Collaborating Sponsors:

Genentech, Inc.

Conditions:

Cystic Fibrosis

Eligibility:

All Genders

1-30 years

Phase:

PHASE2

Brief Summary

This is a study to find out whether Pulmozyme is effective for clearing mucus from the airways of children with cystic fibrosis less than 3 ½ years of age.

Detailed Description

Pulmozyme is given using a nebulizer and is now widely used in older children and adults with cystic fibrosis. In adults and older children, studies have shown that daily use of Pulmozyme improves lun...

Eligibility Criteria

Inclusion

  • Age \< 30 months
  • Diagnosis of CF based on clinical features consistent with CF as well as 1 of the 2 following criteria: a) two sweat chlorides \>60 mEq/L (by quantitative pilocarpine iontophoresis), b) genotype with 2 identifiable mutations consistent with CF.
  • Informed consent by parent or legal guardian

Exclusion

  • Previous treatment with Pulmozyme
  • Hospitalization or treatment with IV antibiotics with 14 days of initial study visit
  • Acute intercurrent respiratory infection, defined as any of the following symptoms within the preceding 48 hours: 1) fever \> 38 degrees C, 2) new onset of coryza or other upper respiratory symptoms, 3) increase in cough, wheezing, or respiratory rate
  • History of adverse reaction to sedation
  • Oxyhemoglobin saturation \<90% on room air
  • Severe upper airway obstruction as determined by site PI (severe laryngomalacia, markedly enlarged tonsils, significant snoring, diagnosed obstructive sleep apnea)
  • Hemodynamically significant congenital heart disease or diagnosed arrhythmias
  • History of hemoptysis
  • History of previous pulmonary air leak (pneumothorax)
  • Diagnosed seizure disorder necessitating current anticonvulsive therapy. A history of febrile seizures is not an exclusion criterion.
  • Use of Investigational drug(s) within 60 days or 5 half-lives of enrollment in this study.
  • Known allergy to Chinese Hamster Ovary-derived biological products or any component of the placebo or active drug formulations.

Key Trial Info

Start Date :

January 1 2005

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

July 1 2016

Estimated Enrollment :

24 Patients enrolled

Trial Details

Trial ID

NCT00179998

Start Date

January 1 2005

End Date

July 1 2016

Last Update

May 9 2019

Active Locations (1)

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Page 1 of 1 (1 locations)

1

Nationwide Children's Hospital

Columbus, Ohio, United States, 43205