Status:

COMPLETED

The Effect of Diflunisal on Familial Amyloidosis

Lead Sponsor:

Boston University

Collaborating Sponsors:

Food and Drug Administration (FDA)

National Institute of Neurological Disorders and Stroke (NINDS)

Conditions:

Familial Amyloid Polyneuropathy

Familial Amyloidosis

Eligibility:

All Genders

18-75 years

Phase:

PHASE2

PHASE3

Brief Summary

The purpose of this study is to determine if diflunisal can prevent progressive lower leg nerve damage in patients with familial amyloidosis polyneuropathy. Funding Source - FDA Office of Orphan Prod...

Detailed Description

Familial amyloidosis polyneuropathy (FAP) is a rare, lethal, autosomal dominant, neurodegenerative disease characterized by misfolding of variant transthyretin tetramer (TTR) - a transport protein pro...

Eligibility Criteria

Inclusion

  • Age 18 to 75 years
  • Biopsy proven amyloidosis
  • Genotyping of variant transthyretin
  • Signs of peripheral or autonomic neuropathy

Exclusion

  • Use of other non-steroidal anti-inflammatory drugs
  • Other causes of sensorimotor polyneuropathy
  • Anticipated survival \<2 years or liver transplantation in \<1 yr
  • Liver transplantation
  • Profound nerve, heart or kidney impairment
  • Pregnancy or unwillingness to use contraception by women of childbearing age
  • Active or recent gastrointestinal bleeding
  • Non-steroidal or aspirin drug allergy/hypersensitivity

Key Trial Info

Start Date :

February 1 2006

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

December 1 2012

Estimated Enrollment :

130 Patients enrolled

Trial Details

Trial ID

NCT00294671

Start Date

February 1 2006

End Date

December 1 2012

Last Update

March 17 2017

Active Locations (8)

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Page 1 of 2 (8 locations)

1

Amyloidosis Center, Boston Medical Center

Boston, Massachusetts, United States, 02118

2

Mayo Clinic Rochester

Rochester, Minnesota, United States, 55905

3

Mount Sinai School of Medicine, Department of Medicine

New York, New York, United States, 10029-6574

4

IRCCS Policlinico San Matteo

Pavia, Italy, 27100