Status:

COMPLETED

The Effects of Kuvan on Functional Brain Connectivity in Individuals With Phenylketonuria (PKU)

Lead Sponsor:

University of Missouri-Columbia

Collaborating Sponsors:

BioMarin Pharmaceutical

Conditions:

Phenylketonuria

Eligibility:

All Genders

6+ years

Brief Summary

The objective of the study is to determine whether Kuvan™ (sapropterin) improves the strength of the functional connectivity between brain regions in individuals with PKU.

Detailed Description

The proposed study is designed to evaluate the hypothesis that functional connectivity may represent an early marker for neurocognitive improvements related to Kuvan treatment. As a first step in the ...

Eligibility Criteria

Inclusion

  • Willing and able to provide informed consent or assent.
  • Willing and able to comply with study procedures.
  • Greater than or equal to 6 years of age.
  • For phenylketonuria, intention of physician to prescribe sapropterin.
  • For phenylketonuria, phenylalanine level greater than or equal to 300μmol/L.
  • For phenylketonuria, negative pregnancy test if of childbearing potential.
  • For phenylketonuria, willing to use contraception if sexually active.

Exclusion

  • Pregnant, breastfeeding, or planning to become pregnant during study.
  • Use of investigational product less than 30 days prior to or during study.
  • Concurrent condition that could interfere with participation or safety.
  • Any condition creating high risk of poor compliance with study.
  • Perceived to be unreliable or unavailable for study.
  • Use of L-Dopa, methotrexate, or other drugs that inhibit folate metabolism.
  • For phenylketonuria, known hypersensitivity to sapropterin or excipients.

Key Trial Info

Start Date :

August 1 2009

Trial Type :

OBSERVATIONAL

Allocation :

ACTUAL

End Date :

August 1 2011

Estimated Enrollment :

20 Patients enrolled

Trial Details

Trial ID

NCT00964236

Start Date

August 1 2009

End Date

August 1 2011

Last Update

January 4 2018

Active Locations (1)

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Page 1 of 1 (1 locations)

1

University of Missouri

Columbia, Missouri, United States, 65211