Status:

COMPLETED

Phase 3 Study of Cysteamine Bitartrate Delayed-release (RP103) Compared to Cystagon® in Patients With Cystinosis

Lead Sponsor:

Amgen

Conditions:

Cystinosis

Eligibility:

All Genders

6+ years

Phase:

PHASE3

Brief Summary

Cystinosis is an inherited disease that if untreated, results in kidney failure as early as the first decade of life. The current marketed therapy is Cystagon® (cysteamine bitartrate) which must be ta...

Detailed Description

This is a multi-center, open-label, randomized, cross-over study to determine whether steady-state, twice a day treatment with Cysteamine Bitartrate Delayed-release Capsules(RP103) results in comparab...

Eligibility Criteria

Inclusion

  • Male and female subjects must have nephropathic cystinosis.
  • Subjects must be on a stable dose of Cystagon® sufficient to maintain their white blood cell (WBC) cystine level at ≤ 1.0 nmol/half-cystine/mg protein.
  • Subjects must be able to swallow their typically administered Cystagon® capsule with the capsule intact.
  • Within the last 6 months, no clinically significant change in liver function \[i.e., ALT, AST, total bilirubin\] and renal function \[i.e., estimated GFR\] at Screening as determined by the Investigator.
  • Subjects with an estimated GFR (corrected for body surface area) \> 30 mL/min/1.73m2.
  • Sexually active female subjects of childbearing potential (i.e., not surgically sterile \[tubal ligation, hysterectomy, or bilateral oophorectomy\] or at least 2 years naturally postmenopausal) must agree to utilize the same acceptable form of contraception from Screening through completion of the study.
  • Subjects must be willing and able to comply with the study restrictions and requirements.
  • Subjects or their or their parent or guardian must provide written informed consent and assent (where applicable) prior to participation in the study.

Exclusion

  • Subject's age \< 6 years old or subject's weight \< 21 kg.
  • Subjects with a known history, currently of the following conditions or other health issues that make it, in the opinion of the investigator, unsafe for them to participate: inflammatory bowel disease (if currently active) or have had prior resection of small intestine; Heart disease (e.g., myocardial infarction, heart failure, arrhythmias or poorly controlled hypertension) 90 days prior to Screening; Active bleeding disorder 90 days prior to Screening; Malignant disease within the last 2 years.
  • Patients with a hemoglobin level \< 10 g/dL at Screening or a level that, in the opinion of the investigator, makes it unsafe for the subject to participate.
  • Subjects receiving any form of cysteamine medication through a gastric tube.
  • Subjects who are receiving maintenance dialysis or who have had a kidney transplant.
  • Subjects who are on an active kidney transplant list or who are planning to receive a kidney transplant within 3 months of Screening.
  • Subjects with known hypersensitivity to cysteamine or penicillamine.
  • Female subjects who are nursing, planning a pregnancy, known or suspected to be pregnant, or have a positive serum pregnancy screen.
  • Subjects who have a made a blood donation within 30 days of Screening.
  • Subjects who, in the opinion of the Investigator, are not able or willing to comply with the protocol.

Key Trial Info

Start Date :

June 1 2010

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

August 1 2011

Estimated Enrollment :

43 Patients enrolled

Trial Details

Trial ID

NCT01000961

Start Date

June 1 2010

End Date

August 1 2011

Last Update

December 19 2024

Active Locations (8)

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Page 1 of 2 (8 locations)

1

Stanford University Medical School

Stanford, California, United States, 94305

2

Emory Children's Center

Atlanta, Georgia, United States, 30322

3

Ann & Robert H. Lurie Children's Hospital of Chicago (formerly Children's Memorial Hospital)

Chicago, Illinois, United States, 60614

4

Hospices Civils de Lyon

Lyon, France