Status:

TERMINATED

The Natural History of Reproductive and Overall Health in Girls and Women With a Pre-Mutation in the FMR1 Gene; Creation of a Patient Registry

Lead Sponsor:

Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD)

Conditions:

Fragile X Syndrome

FMR1 Premutation

Eligibility:

FEMALE

18+ years

Brief Summary

Background: * In human DNA, the Fragile X (FMR1) gene helps to regulate the nervous and reproductive systems. If the gene is abnormal, it can cause different kinds of problems, such as abnormal menst...

Detailed Description

Spontaneous 46,XX primary ovarian insufficiency (POI) is a cause of decreased fertility in approximately 1% of women before age 40. The most common known genetic cause of 46,XX POI is a pre -mutation ...

Eligibility Criteria

Inclusion

  • INCLUSION CRITERIA:
  • Women ages 18 and older
  • FMR1 CGG repeats numbering between 55 and 199, as determined by standard Southern blot and PCR techniques.
  • EXCLUSION CRITERIA:
  • Males
  • Children
  • Women who do not have an FMR1 pre-mutation (CGG repeat number \<55 or \>199)
  • Inability to make personal medical decisions
  • CRITERIA FOR SCREENING FOR THE FMR1 PRE-MUTATION:
  • Family history of Fragile X syndrome or mental retardation
  • Personal or family history of primary ovarian insufficiency (or POF or premature menopause )
  • Personal or famiy history of tremor ataxia syndrome or Parkinson s disease

Exclusion

    Key Trial Info

    Start Date :

    August 5 2010

    Trial Type :

    OBSERVATIONAL

    Allocation :

    ACTUAL

    End Date :

    May 31 2013

    Estimated Enrollment :

    7 Patients enrolled

    Trial Details

    Trial ID

    NCT01187524

    Start Date

    August 5 2010

    End Date

    May 31 2013

    Last Update

    October 6 2017

    Active Locations (1)

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    Page 1 of 1 (1 locations)

    1

    National Institutes of Health Clinical Center, 9000 Rockville Pike

    Bethesda, Maryland, United States, 20892