Status:

TERMINATED

The NIH UNI Study: Urea Cycle Disorders, Nutrition and Immunity

Lead Sponsor:

National Human Genome Research Institute (NHGRI)

Conditions:

Argininosuccinic Aciduria

Carbamoyl-Phosphate Synthase I Deficiency

Eligibility:

All Genders

2-99 years

Brief Summary

Objectives: * To study nutrition and immune system problems in people with urea cycle disorders. * To study how people with urea cycle disorders and healthy volunteers respond to standard flu and/or ...

Detailed Description

Urea cycle disorders (UCD) are amongst the most frequent of the inborn errors of metabolism (IEM) and result from a block in the hepatic disposal of waste nitrogen from protein catabolism. Viral infec...

Eligibility Criteria

Inclusion

  • INCLUSION CRITERIA:
  • Patients:
  • Any gender and ethnicity age 2 years and older with a diagnosis of a urea cycle disorder are eligible to enroll in this protocol.
  • Patients need to be medically and nutritionally managed by a local metabolic provider. If necessary, we will obtain written consent from the patient to review medical records from their home physician to confirm eligibility.
  • Healthy Volunteers:
  • Any gender and ethnicity age 2 years and older are eligible to enroll in this protocol.
  • Have access to own personal medical provider \<TAB\>
  • EXCLUSION CRITERIA:
  • Less than 2 years of age
  • Inability to travel to NIH because of their medical condition
  • Recent (6 month) history of vaccination or immune modulating drug
  • Severe reactions to eggs and or latex
  • History of severe reactions to previous immunizations (e.g. hives, rash, difficulty breathing)
  • Persons without a personal medical provider
  • Persons with current infections or under care of medical provider for an ongoing medical issue

Exclusion

    Key Trial Info

    Start Date :

    August 8 2011

    Trial Type :

    OBSERVATIONAL

    Allocation :

    ACTUAL

    End Date :

    April 17 2013

    Estimated Enrollment :

    4 Patients enrolled

    Trial Details

    Trial ID

    NCT01421888

    Start Date

    August 8 2011

    End Date

    April 17 2013

    Last Update

    December 9 2019

    Active Locations (1)

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    Page 1 of 1 (1 locations)

    1

    National Institutes of Health Clinical Center, 9000 Rockville Pike

    Bethesda, Maryland, United States, 20892