Status:

UNKNOWN

Susceptibility to Infections, Tumor Risk and Liver Disease in Patients With Ataxia Telangiectasia

Lead Sponsor:

Johann Wolfgang Goethe University Hospital

Conditions:

Ataxia Telangiectasia

Eligibility:

All Genders

2-45 years

Phase:

NA

Brief Summary

Ataxia telangiectasia (A-T) is a rare devastating human recessive disorder characterized by progressive cerebellar ataxia, immunodeficiency, chromosomal instability and cancer susceptibility. The immu...

Detailed Description

Ataxia teleangiectasia (A-T) is a rare devastating human recessive disorder characterized by progressive cerebellar ataxia, immunodeficiency, chromosomal instability and cancer susceptibility. The imm...

Eligibility Criteria

Inclusion

  • aim group: genetically and/or clinically diagnosed A-T
  • age 2-45 years
  • written informed consent

Exclusion

  • age \< 2 or \> 45 years
  • other diseases with influence on the immune system (i.e. diabetes mellitus, malignoma, dialysis-dependent renal failure)

Key Trial Info

Start Date :

October 1 2016

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

September 30 2019

Estimated Enrollment :

30 Patients enrolled

Trial Details

Trial ID

NCT03357978

Start Date

October 1 2016

End Date

September 30 2019

Last Update

November 30 2017

Active Locations (1)

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1

Children's Hospital, Allergology, Pneumology and Cystic Fibrosis, Goethe University Frankfurt

Frankfurt am Main, Hesse, Germany, 60590