Status:

RECRUITING

Mechanisms of Familial Pulmonary Fibrosis

Lead Sponsor:

Vanderbilt University Medical Center

Conditions:

Familial Pulmonary Fibrosis

Idiopathic Pulmonary Fibrosis

Eligibility:

All Genders

40-75 years

Brief Summary

This a prospective, longitudinal study of first-degree family members of patients diagnosed with familial interstitial pneumonia (FIP). FIP is the familial form of idiopathic pulmonary fibrosis (IPF),...

Detailed Description

Potential research subjects will be sent a questionnaire (modified version of the ATS-DLD-78 questionnaire) and study consent form. Individuals with no prior history of lung disease and a dyspnea scor...

Eligibility Criteria

Inclusion

  • Eligibility Requirements:
  • Bloodline members of an affected individual from a family in which two or more members of a family are known to have Idiopathic Interstitial Pneumonia (IIP) and who have no personal diagnosis of IIP or IPF
  • Sibling or adult child of an affected individual
  • Exclusion Criteria:
  • Inability to understand the requirements of the study or be unwilling to provide written informed consent (as evidenced by signature on an informed consent document approved by the IRB).
  • Inability to travel to Nashville for 1-2 outpatient visits and/or complete a written or online version of the Interstitial Lung Disease Questionnaire
  • Age \< 40 or \>75 years old. If the affected relative was younger than 50 years old at the time of IIP diagnosis, potential subjects between age 18 and 40 years may participate when they are up to 10 years younger than the age at relative's diagnosis.
  • Underlying disease with signs and symptoms that could be confused with IIP or IPF symptoms (i.e., rheumatoid arthritis or other connective tissue diseases, occupational lung disease, chemotherapy, etc.)
  • Thought to be unsuitable for participation in the study in the opinion of the investigator

Exclusion

    Key Trial Info

    Start Date :

    January 1 2009

    Trial Type :

    OBSERVATIONAL

    Allocation :

    ESTIMATED

    End Date :

    January 30 2030

    Estimated Enrollment :

    750 Patients enrolled

    Trial Details

    Trial ID

    NCT03437486

    Start Date

    January 1 2009

    End Date

    January 30 2030

    Last Update

    December 31 2025

    Active Locations (1)

    Enter a location and click search to find clinical trials sorted by distance.

    Page 1 of 1 (1 locations)

    1

    Vanderbilt University Medical Center

    Nashville, Tennessee, United States, 37232