Status:

TERMINATED

Open Label, Study Of Efficacy and Safety Of AVR-RD-01 for Treatment-Naive Subjects With Classic Fabry Disease

Lead Sponsor:

AVROBIO

Conditions:

Fabry Disease

Eligibility:

MALE

16-50 years

Phase:

PHASE1

PHASE2

Brief Summary

This was a multinational, open-label study to assess the efficacy and safety of AVR-RD-01 in approximately 15 male subjects, who were 16 years of age or older and postpubertal with a confirmed diagnos...

Detailed Description

The duration of each subject's participation in this study was approximately 64 weeks (or 1 year, 12 weeks), comprised of five study periods (Screening, Baseline, Pre-transplant, Transplant, and Post-...

Eligibility Criteria

Inclusion

  • Subject was male, 16 years of age or older (18 years of age or older in the US), and post pubertal,(minimum age by region)
  • Subject had a confirmed diagnosis of classic Fabry disease based on deficient AGA enzyme activity (defined as \< 1% of normal).

Exclusion

  • Subject had a galactosidase alpha (GLA) gene mutation associated with late-onset cardiac variant Fabry disease.
  • Subject had previously received ERT and/or chaperone therapy within 3 years for treatment of Fabry disease.
  • Subject had tested positive for anti-AGA antibodies at the time of screening.
  • Subject had eGFR \< 60 mL/min/1.73 m² (ie, chronic kidney disease \[CKD\] stage ≥ 3) at Screening.
  • Subject had a prior history of myocardial infarction (MI).
  • Subject had a history of coronary artery disease (CAD) with angina requiring percutaneous transluminal coronary angioplasty (with or without stent placement) and/or coronary artery bypass graft (CABG).
  • Subject had a history of moderate to severe valvular heart disease requiring valve replacement.
  • Subject had a history of heart failure, moderate to severe diastolic dysfunction, and/or left ventricular ejection fraction (LVEF) ≤ 45% on echocardiogram (ECHO) performed at rest at Screening.
  • Subject had a history of clinically significant cardiac arrhythmia (eg, heart block \[second or third degree\], atrial fibrillation requiring therapy, ventricular fibrillation, ventricular tachycardia, supraventricular tachycardia, or cardiac arrest).
  • Note \[history of intermittent atrial fibrillation not requiring treatment was allowed\].
  • Subject had a prior history of stroke and/or transient ischemic attack (TIA).
  • Subject had aspartate aminotransferase (AST) and/or alanine aminotransferase (ALT) ≥ 3 times the upper limit of normal (ULN) at Screening.
  • Subject had a prior history of (or current) malignancy; the one exception is a prior history of resected basal cell carcinoma.
  • Subject had previously received treatment with AVR-RD-01 or any other gene therapy.
  • Other inclusion/exclusion criteria apply.

Key Trial Info

Start Date :

February 21 2018

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

March 14 2022

Estimated Enrollment :

15 Patients enrolled

Trial Details

Trial ID

NCT03454893

Start Date

February 21 2018

End Date

March 14 2022

Last Update

January 5 2024

Active Locations (5)

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Page 1 of 2 (5 locations)

1

Hackensack University Medical Center

Hackensack, New Jersey, United States, 07601

2

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, United States, 15213

3

Royal Melbourne Hospital

Melbourne, Parkville VIC, Australia

4

Royal Perth Hospital

Perth, Australia