Status:

COMPLETED

Orkambi Treatment in 2 to 5 Year Old Children With CF

Lead Sponsor:

Children's Hospital of Philadelphia

Collaborating Sponsors:

Vertex Pharmaceuticals Incorporated

Conditions:

Cystic Fibrosis

Eligibility:

All Genders

2-5 years

Brief Summary

The purpose of this observational research study is to determine the effects of clinically prescribed Orkambi treatment on 2 to 5 year old children homozygous for the F508del Mutations in the Cystic f...

Detailed Description

Orkambi is a novel FDA approved (August, 2018) therapy for use in patients with cystic fibrosis (CF) who are 2 to 5 years of age and homozygous for F508del mutations in the CFTR gene. It is a combinat...

Eligibility Criteria

Inclusion

  • Cystic fibrosis and homozygous for F508del mutations, approved for treatment
  • Age: 2.0 to 5.9 years
  • In usual state of good health
  • A clinical decision has been made for subject to begin Orkambi treatment
  • Family committed to the 6 to 8 month study protocol with visits to the Children's Hospital of Philadelphia (CHOP) that will last 2-3 days for the baseline visit (Visit 1) prior to Orkambi and the 24 week visit (Visit 3) after clinically prescribed Orkambi treatment has begun, and will last up to 2 days for the 12 week visit (Visit 2) after Orkambi treatment has begun.

Exclusion

  • On parenteral nutrition
  • Use of any medications that inhibit or induce cytochrome P450 (CYP) 3A
  • Liver function tests elevated above 3x the reference range for age and sex
  • Lung disease considered severe based on clinical impression by home CF center.
  • Other illness affecting growth or nutritional status
  • Other contraindications described for Orkambi therapy

Key Trial Info

Start Date :

April 10 2019

Trial Type :

OBSERVATIONAL

Allocation :

ACTUAL

End Date :

June 16 2021

Estimated Enrollment :

28 Patients enrolled

Trial Details

Trial ID

NCT03795363

Start Date

April 10 2019

End Date

June 16 2021

Last Update

December 2 2021

Active Locations (1)

Enter a location and click search to find clinical trials sorted by distance.

Page 1 of 1 (1 locations)

1

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States, 19146