Status:

TERMINATED

Assessing Clinical Endpoints and Biomarkers in Myotonic Dystrophy Type-1 and Type 2 (ASCEND-DM)

Lead Sponsor:

National Institute of Neurological Disorders and Stroke (NINDS)

Conditions:

Myotonic Dystrophy Type-1

Myotonic Dystrophy Type-2

Eligibility:

All Genders

11-70 years

Brief Summary

Background: Myotonic dystrophy is a long-term genetic disorder that affects muscle function. Symptoms include gradually worsening muscle loss and weakness. Muscles often contract and cannot relax. Re...

Detailed Description

Objective: Myotonic dystrophy type 1 (DM1) and type 2 (DM2) are the most common inherited skeletal myopathies in adults. RNA toxicity is the core disease mechanism, good molecular targets have been id...

Eligibility Criteria

Inclusion

  • INCLUSION CRITERIA:
  • Age 11 to 70 inclusive
  • Competent to provide informed consent and assent (consent of a parent or guardian will be required for pediatric participants)
  • Positive genetic test for DM1 or DM2 (Genetic testing for DM1 or DM2 may be determined after enrollment
  • EXCLUSION CRITERIA:
  • Concurrent enrollment in a clinical trial or participation in an investigative drug trial within 6 months of study entry.
  • Concurrent pregnancy or planned pregnancy during the course of the study.
  • Concurrent medical condition that would, in the opinion of the investigator or clinical evaluator, compromise performance on study measures:
  • Clinically significant infections or medical illness within 30 days from study entry.
  • History of, or abnormal laboratory values indicative of, significant medical, neurologic (other than DM1 or DM2), or psychiatric disorders.
  • A recent history (30 days prior to study entry) of any of the following conditions on routine blood screening: white blood cells \< 3000, platelets \< 100,000, hematocrit \< 30%, symptomatic liver disease with serum albumin \< 3 g/L, or creatinine \> 1.5 mg%.
  • Any of the following medical conditions: uncontrolled or insulin-dependent diabetes mellitus, congestive heart failure, symptomatic cardiomyopathy, symptomatic coronary artery disease, cancer (other than skin cancer) within 5 years from study entry, multiple sclerosis, or other serious medical illness.
  • Other diseases that mimic the signs or symptoms of DM1 or DM2. Coexistence of other neuromuscular disease.
  • Thyroid dysfunction that is untreated (if on thyroid hormone replacement therapy, need to have adequate and stable replacement over the previous 6 months from study entry).
  • Second or third degree heart block, atrial flutter, atrial fibrillation, ventricular tachycardia, or is receiving medication for the treatment of cardiac arrhythmia.
  • Liver or kidney disease requiring ongoing treatment.
  • Have a seizure disorder.
  • Drug or alcohol abuse within 3 months of study entry (DSM-V criteria will be used for the diagnosis and level of a substance use disorder:
  • Treatment with supplemental anabolic hormones (including testosterone, human recombinant growth hormone, human recombinant insulin like growth factor-1, other anabolic drug mixtures) during the previous 12 months from study entry.
  • Note: non-ambulatory participants are not excluded but are limited to \<15% of enrollment. Individuals using a cane or walker will not be examined for gait, balance and mobility.

Exclusion

    Key Trial Info

    Start Date :

    February 24 2020

    Trial Type :

    OBSERVATIONAL

    Allocation :

    ACTUAL

    End Date :

    November 2 2021

    Estimated Enrollment :

    4 Patients enrolled

    Trial Details

    Trial ID

    NCT03867435

    Start Date

    February 24 2020

    End Date

    November 2 2021

    Last Update

    November 4 2021

    Active Locations (1)

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    Page 1 of 1 (1 locations)

    1

    National Institutes of Health Clinical Center

    Bethesda, Maryland, United States, 20892

    Assessing Clinical Endpoints and Biomarkers in Myotonic Dystrophy Type-1 and Type 2 (ASCEND-DM) | DecenTrialz