Status:

RECRUITING

Cystic Fibrosis Transmembrane Regulator (CFTR) Biomarker Study to Evaluate the Rescue of Mutant CFTR in Patients With Cystic Fibrosis Treated With CFTR-modulators

Lead Sponsor:

Charite University, Berlin, Germany

Collaborating Sponsors:

Hannover Medical School

Heidelberg University

Conditions:

Cystic Fibrosis

Eligibility:

All Genders

6+ years

Brief Summary

This observational study evaluates the effect of therapy with cystic fibrosis transmembrane regulator (CFTR) modulators on CFTR function measured by the CFTR biomarker intestinal current measurement (...

Detailed Description

Cystic fibrosis transmembrane regulator (CFTR) biomarker (intestinal current measurement (ICM), nasal potential difference (NPD), sweat chloride) before the start of therapy and 12 and 52 weeks after ...

Eligibility Criteria

Inclusion

  • Decision for cystic fibrosis (CF) transmembrane regulator (CFTR)-modulator therapy by the patient and the caring CF physician
  • Signed informed consent form (ICF) and, where appropriate, signed assent form.

Exclusion

  • Ongoing participation in an investigational drug study (including studies investigating lumacaftor, tezacaftor or ivacaftor)

Key Trial Info

Start Date :

July 1 2018

Trial Type :

OBSERVATIONAL

Allocation :

ESTIMATED

End Date :

December 31 2027

Estimated Enrollment :

200 Patients enrolled

Trial Details

Trial ID

NCT04732910

Start Date

July 1 2018

End Date

December 31 2027

Last Update

March 4 2024

Active Locations (4)

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Page 1 of 1 (4 locations)

1

Charité - Universitätsmedizin Berlin

Berlin, Germany, 13353

2

Justus-Liebig-University Giessen

Giessen, Germany

3

Hannover Medical School

Hanover, Germany

4

University of Heidelberg

Heidelberg, Germany