Status:

COMPLETED

Testing Miglustat Administration in Subjects With Spastic Paraplegia 11

Lead Sponsor:

IRCCS Fondazione Stella Maris

Conditions:

Hereditary Spastic Paraparesis

Eligibility:

All Genders

14+ years

Phase:

PHASE2

Brief Summary

Hereditary spastic paraparesis type 11 (SPG11) is caused by mutations in the SPG11 gene that produces spatacsin, a protein involved in lysosomal function. Studies performed in skin cells (fibroblasts)...

Detailed Description

We will analyze the safety of Miglustat

Eligibility Criteria

Inclusion

  • Written signed informed consent;
  • Confirmed diagnosis of SPG11;
  • Age \> 13 years;
  • SPRS score ≥ 10 or ≤35;
  • Use of effective contraceptive methods and the performance of pregnancy tests (only fertile subjects).

Exclusion

  • Diagnosis of other concomitant neurodegenerative diseases;
  • Outcomes of severe pre- or peri-natal suffering;
  • Age ≤ 13 years;
  • SPRS score ≥ 35 or ≤10;
  • Hypersensitivity or intolerance to miglustat;
  • Participation in other pharmacological studies within 30 days of the first Study visit (T0);
  • The inability to take the drug;
  • Any additional medical conditions;
  • Subjects with severe renal impairment;
  • Refusal to use effective contraceptive methods and the performance of pregnancy tests (only fertile subjects).

Key Trial Info

Start Date :

June 15 2021

Trial Type :

INTERVENTIONAL

Allocation :

ACTUAL

End Date :

September 15 2021

Estimated Enrollment :

10 Patients enrolled

Trial Details

Trial ID

NCT04768166

Start Date

June 15 2021

End Date

September 15 2021

Last Update

April 11 2022

Active Locations (1)

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1

IRCCS Fondazione Stella Maris

Pisa, PI, Italy, 56128