Status:

UNKNOWN

Evaluation of Adenosine Deaminase (ADA) Enzyme Deficiency in Patients With Lymphopenia and/or Elevated Immunoglobulin E

Lead Sponsor:

TRPHARM

Conditions:

Adenosine Deaminase Deficiency

Eligibility:

All Genders

18-40 years

Brief Summary

This study was designed as an observational, prospective, epidemiological screening study. Patients who have been admitted to the center and whose lymphopenia and/or Immunoglobulin E elevation has bee...

Detailed Description

Primary immunodeficiencies are encountered with signs and symptoms related to various disciplines of medicine and are detected more often in our country than in other societies. Severe Combined Immun...

Eligibility Criteria

Inclusion

  • 1\. Signing of the written informed consent form by the patient and/or his legal representative,
  • The patient is between 18 and 40 years of age.
  • Patients with one major and one minor criteria from the following criteria will be included in the study:
  • Major Criteria:
  • Lymphopenia: The patient has lymphopenia as a result of at least one hemogram,
  • The number of lymphocytes is below 1500/mm3
  • Immunoglobulin E height: The level of immunoglobulin E is above 120 kU/L.
  • Minor Criteria:
  • Two or more new ear infections within a year
  • Two or more new sinus infections within a year when there is no allergy
  • One pneumonia per year for more than a year
  • Chronic diarrhea with weight loss
  • Recurrent viral infections (Colds, herpes, warts, condyloma)
  • The need for repeated intravenous antibiotics to clear infections
  • Recurrent deep skin or internal organ abscesses
  • Persistent thrush or fungal infection of the skin or other place
  • Infection caused by tuberculosis-like bacteria that is normally harmless
  • Primary immunodeficiency in the family

Exclusion

  • Having used drugs that can cause lymphopenia before being included in the study (chemotherapy, cytotoxic drug use, etc.),
  • The Ministry of Health COVID-19 diagnosis guide (nazofaringeal, nasal orofaringiyal or SARS-CoV-2 RNA PCR test and/or tomographic) as COVID-19, diagnosed and/or persons who had contact with patient recruitment criteria, patients diagnosed in this manner karsilasal PCR tests were negative even after those patients in the study will be taken.
  • Before being included in the study, it should be noted that other diseases that can cause lymphopenia (hematological diseases, oncological diseases, etc.) have been diagnosed with,
  • The patient has participated in an interventional clinical trial within the last 30 days,
  • Failure of the patient himself and/or his legal representative to give their consent to participate in the study,
  • According to the researcher's opinion, the patient will not be able to properly fulfill the study requirements,
  • Pregnancy and/or lactation period,
  • The fact that the volunteer participating in

Key Trial Info

Start Date :

December 3 2021

Trial Type :

OBSERVATIONAL

Allocation :

ESTIMATED

End Date :

December 3 2023

Estimated Enrollment :

100 Patients enrolled

Trial Details

Trial ID

NCT05300373

Start Date

December 3 2021

End Date

December 3 2023

Last Update

March 29 2022

Active Locations (1)

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Konya Necmettin Erbakan University

Konya, Meram, Turkey (Türkiye)