Status:

ACTIVE_NOT_RECRUITING

A Study to Evaluate the Safety, Tolerability, PK and PD of Intracerebroventricular GC1123 in Patients with MPS Ⅱ

Lead Sponsor:

GC Biopharma Corp

Conditions:

Mucopolysaccharidosis II

Hunter Syndrome

Eligibility:

All Genders

18-18 years

Phase:

PHASE1

Brief Summary

The purpose of this study is to evaluate the safety, tolerability, pharmacokinetics and pharmacodynamics of intracerebroventricular GC1123 in patients with MPS Ⅱ who have central nervous system involv...

Detailed Description

This study is designed as prospective, open-label, phase I and extension study. Safety, tolerability, pharmacokinetic, and pharmacodynamic properties of repeat-dose treatment of ICV-administered inves...

Eligibility Criteria

Inclusion

  • Patient who has been diagnosed with severe MPS Ⅱ (Hunter syndrome)
  • Patient, aged 1.5 years (18 months) to 18 years at the time of the screening
  • Patient who has received and tolerated a minimum of 12 weeks of treatment with weekly intravenous treatment, and who has received 80% of the total planned infusions within that time frame.
  • Patient who is capable of undergoing neurosurgery, which has been confirmed by neurosurgeons and anesthesiologist.
  • Patient eligible to execute patient evaluation activities during the clinical trial period, as assessed by the investigator
  • Patient whose parents or legal representative are willing to participate in this clinical trial and provide written informed consent form

Exclusion

  • Patient who has been administered with intrathecal Idursulfase in the past
  • Patient with a history of bone marrow transplantation or cord blood transplant
  • Patient with a history of ventriculoperitoneal shunt or other intracranial surgeries
  • Patient with end-stage multiple organ dysfunction syndrome or other severe diseases
  • Patient who is exposed to malignant neoplasm
  • Patient who has received treatment with any investigational drug or device within 30 days prior to study entry
  • Patient who have experience of hypersensitivity or anaphylaxis to ingredients of the investigational product at the time of screening
  • Patient with a history of bronchotomy/tracheostomy, or patient with acute respiratory disease at the time of screening
  • Patient who is ineligible to participate in the clinical trial due to laboratory test results or other reasons, as determined by the investigator

Key Trial Info

Start Date :

September 20 2022

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

June 1 2027

Estimated Enrollment :

12 Patients enrolled

Trial Details

Trial ID

NCT05422482

Start Date

September 20 2022

End Date

June 1 2027

Last Update

October 15 2024

Active Locations (3)

Enter a location and click search to find clinical trials sorted by distance.

Page 1 of 1 (3 locations)

1

Pusan National University Yangsan Hospital

Pusan, South Korea, 50612

2

Seoul National University

Seoul, South Korea, 03080

3

Samsung Medical Center

Seoul, South Korea, 06351