Status:

RECRUITING

Early Discontinuation of Steroid Treatment in Negative FDG-PET/CT Patients With Idiopathic Retroperitoneal Fibrosis

Lead Sponsor:

Assistance Publique - Hôpitaux de Paris

Conditions:

Idiopathic Retroperitoneal Fibrosis

Eligibility:

All Genders

18+ years

Phase:

PHASE4

Brief Summary

Adult patients with a diagnosis of idiopathic retroperitoneal fibrosis Prospective multicentric cohort study Intervention : administration of prednisone during 9 to 21 months at 1mg/kg/day at inclusio...

Detailed Description

At baseline visit: Eligible patients will be screen during a standard visit care (consultation or hospitalization). A clinical examination, an abdominal CT scan, blood and urine biological tests will ...

Eligibility Criteria

Inclusion

  • Patient over 18 years old
  • New onset or untreated relapsing of active idiopathic retroperitoneal fibrosis (IRF) defined by the association of:
  • Related-disease symptoms (Appendix 17.2) or elevated CRP level (\>20 mg/l) AND
  • Retroperitoneal peri-aortic mass that surrounds the abdominal vessels on CT-scan

Exclusion

  • Secondary retroperitoneal fibrosis including drug-related retroperitoneal fibrosis, active infections (such as tuberculosis) or malignancies, systemic vasculitis (such as Anti-neutrophil cytoplasmic autoantibody (ANCA)-associated vasculitis), Erdheim-Chester disease (Appendix 17.3),patients with IgG4 disease may be enrolled
  • Contraindication to perform FDG-PET/CT,
  • Contraindication to perform CT scan with injection of contrast agent,
  • Contraindication to treatment by prednisone
  • Active infection
  • Acute or chronic liver disease that is deemed sufficiently severe to impair their ability to participate in the trial,
  • Active or history of malignancy in last 5 years. Individuals with squamous cell or basal cell skin carcinomas and individuals with cervical carcinoma in situ may be enrolled if they have received curative surgical treatment,
  • Serum creatinine level greater than 400 µmol/L that cannot be attributed to underlying IRF,
  • Live vaccination received from 4 weeks before inclusion,
  • Inhaled glucocorticoids (except for patients with documented asthma),
  • Any previous treatment with rituximab, methotrexate, alemtuzumab, cyclophosphamide, azathioprine, mycophenolate mofetil, infliximab, adalimumab, etanercept within the past 3 months,
  • Pregnancy or breastfeeding,
  • Non-affiliation to a social security regime,
  • Subject deprived of freedom, subject under a legal protective measure
  • Refusal to participate

Key Trial Info

Start Date :

November 25 2022

Trial Type :

INTERVENTIONAL

Allocation :

ESTIMATED

End Date :

November 25 2028

Estimated Enrollment :

41 Patients enrolled

Trial Details

Trial ID

NCT05428826

Start Date

November 25 2022

End Date

November 25 2028

Last Update

May 25 2025

Active Locations (15)

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Page 1 of 4 (15 locations)

1

Médecine Interne

Agen, France, France, 47000

2

Médecine interne

Brest, France, France, 29200

3

Médecine interne et maladies infectieuses - GH Sud Haut Lévêque

Bordeaux, France, 33604

4

Médecine interne - Ambroise Paré

Boulogne-Billancourt, France, 92100