Status:

COMPLETED

Joint and Hematologic Disorders of Noonan Syndrome: French Descriptive Cross-sectional Study

Lead Sponsor:

University Hospital, Brest

Conditions:

Noonan Syndrome

Eligibility:

All Genders

Up to 20 years

Brief Summary

Noonan's syndrome is a rare genetic disease, estimated to be between 1: 1000 to 1: 2500 and characterized by cardiothoracic malformations, sometimes mental retardation, but also by hematologic abnorma...

Detailed Description

Noonan Syndrome is a genetic disease whose prevalence is not clearly defined and would be between 1/1000 and 1/2500. Affected patients have various morphological abnormalities, cardiothoracic malform...

Eligibility Criteria

Inclusion

  • Patients ≤ 20 years at the time of diagnosis
  • Noonan syndrome confirmed by van der Burgt score
  • At least one consultation in the participating center

Exclusion

  • Patient \> 20 years old at the time of diagnosis
  • Absence of diagnostic criteria for van der Burgt's Noonan syndrome
  • Other rasopathies
  • Genetic mutations of MEK1, MEK2 and HRAS (which are associated with cardi-faci-cutaneous syndrome and Costello syndrome)
  • Refusal of participation in the study

Key Trial Info

Start Date :

July 2 2019

Trial Type :

OBSERVATIONAL

Allocation :

ACTUAL

End Date :

March 28 2020

Estimated Enrollment :

71 Patients enrolled

Trial Details

Trial ID

NCT06550635

Start Date

July 2 2019

End Date

March 28 2020

Last Update

August 13 2024

Active Locations (4)

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Page 1 of 1 (4 locations)

1

CHRU de Brest

Brest, France, 29609

2

CHU de Caen

Caen, France, 14033

3

CHU de Nantes

Nantes, France, 44093

4

CHU de Toulouse

Toulouse, France, 31000